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Betty Y L Hsu

Explore the profile of Betty Y L Hsu including associated specialties, affiliations and a list of published articles. Areas
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Citations 80
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Recent Articles
1.
Li C, Matter A, Kelly A, Petty T, Najafi H, MacMullen C, et al.
J Biol Chem . 2006 Apr; 281(22):15064-72. PMID: 16574664
Glutamate dehydrogenase (GDH) plays an important role in insulin secretion as evidenced in children by gain of function mutations of this enzyme that cause a hyperinsulinism-hyperammonemia syndrome (GDH-HI) and sensitize...
2.
Cederbaum S, Koo-McCoy S, Tein I, Hsu B, Ganguly A, Vilain E, et al.
Mol Genet Metab . 2002 Nov; 77(3):195-201. PMID: 12409266
Three older patients were diagnosed with systemic carnitine deficiency in childhood nearly a generation ago and have together been treated for more than 50 patient years. Treatment improved tissue carnitine...
3.
Fang J, Hsu B, MacMullen C, Poncz M, Smith T, Stanley C
Biochem J . 2002 Mar; 363(Pt 1):81-7. PMID: 11903050
Glutamate dehydrogenase (GDH) catalyses the reversible oxidative deamination of l-glutamate to 2-oxoglutarate in the mitochondrial matrix. In mammals, this enzyme is highly regulated by allosteric effectors. The major allosteric activator...