[Multiple Familiar Trichoepithelioma (Brooke's Syndrome) : A Rare Autosomal Dermatosis with Possible Periocular Manifestation]

Overview

Journal Ophthalmologe

Specialty Ophthalmology

Date 2008 Oct 3

PMID 18830600

Authors

F Rensch

B Harder

M Goebeler

W Back

J B Jonas

F Schlichtenbrede

Affiliations

Soon will be listed here.

Abstract

Brooke's syndrome is a rare autosomal dominant dermatosis characterized by multiple trichoepitheliomas, which preferentially arise in the face. Therapy consists of excisional surgery of larger tumors and for multiple lesions, dermal abrasion or laser therapy may be considered. Patients with Brooke's syndrome should be closely followed-up due to the possible development of malignant skin tumours. Here, we present a patient with Brooke's syndrome and report on the course of treatment.

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