Multiple Hereditary Trichoepithelioma and Cylindroma (Brooke-Spiegler Syndrome)

Overview

Journal Dermatologica

Publisher Karger

Specialty Dermatology

Date 1991 Jan 1

PMID 1660416

Citations 2

Authors

M Delfino

F DAnna

S Ianniello

V DOnofrio

Affiliations

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Abstract

Three cases of trichoepithelioma associated with cylindroma (Brooke-Spiegler syndrome) in the same family are reported. Three generations were affected. The syndrome usually beginning at puberty is inherited as an irregular autosomal dominant trait.

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