Article: Carcinoid tumour of the ampulla of Vater associated with cutaneous neurofibromatosis

A case of carcinoid tumour of Vater's ampulla is described from a patient with widespread cutaneous neurofibromatosis. The literature concerning the few known cases of carcinoids occurring at this site is briefly reviewed and the presentation, prognosis and treatment discussed, together with the possible significance of such a clinical association.

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Carcinoid Tumour of the Ampulla of Vater Associated with Cutaneous Neurofibromatosis