Multiple Endocrine Neoplasia Associated with Von Recklinghausen's Disease

Overview

Journal Br Med J (Clin Res Ed)

Specialty General Medicine

Date 1983 Nov 5

PMID 6139138

Citations 7

Authors

D F Griffiths

G T Williams

E D Williams

Affiliations

Soon will be listed here.

Abstract

Details were studied of three patients with duodenal carcinoid tumour in association with neurofibromatosis and phaeochromocytoma, and of four patients with duodenal carcinoid and either von Recklinghausen's disease or phaeochromocytoma. The rarity of these endocrine tumours, together with the unusual morphological features and somatostatin content of the two duodenal carcinoids examined, suggest that this combination of tumours is not a chance association. It is suggested that this linkage of neurofibromatosis, phaeochromocytoma, and duodenal carcinoid is a specific multiple endocrine neoplasia syndrome.

Citing Articles

Neurofibromatosis 1 presenting with multiple duodenal GISTS associated with a somatostatin-producing D cell neoplasm.

Serio G, Zampatti C, Ballabio A, Ricci R, Martini M, Zurleni F Endocr Pathol. 2013; 24(2):100-5.

PMID: 23564025 DOI: 10.1007/s12022-013-9239-x.

[Von Recklinghausen type I neurofibromatosis and neuroendocrine tumor (somatostatinoma) in a 50-year-old woman].

Reichardt M, Rexroth W, Hasslacher C Med Klin (Munich). 1998; 93(9):550-3.

PMID: 9792022 DOI: 10.1007/BF03042665.

A patient with co-existing bronchial carcinoid tumour and bilateral phaeochromocytoma.

Chan H, Yeung V, Chow C, Ko G, Cockram C Postgrad Med J. 1995; 71(832):102-3.

PMID: 7724418 PMC: 2397942. DOI: 10.1136/pgmj.71.832.102.

The clinical and laboratory correlates of an increased urinary 5-hydroxyindoleacetic acid.

Tormey W, FitzGerald R Postgrad Med J. 1995; 71(839):542-5.

PMID: 7479466 PMC: 2398246. DOI: 10.1136/pgmj.71.839.542.

Glandular duodenal carcinoid--a somatostatin rich tumour with neuroendocrine associations.

Griffiths D, Jasani B, Newman G, Williams E, Williams G J Clin Pathol. 1984; 37(2):163-9.

PMID: 6141184 PMC: 498672. DOI: 10.1136/jcp.37.2.163.

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