Weber-Christian Panniculitis and Auto-immune Disease: a Case Report

Overview

Journal J Clin Pathol

Specialty Pathology

Date 1976 Feb 1

PMID 777034

Citations 11

Authors

T G Allen-Mersh

Affiliations

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Abstract

A case is described of Weber-Christian panniculitis accompanied by a gammaglobulin disturbance which preceded by five years the diagnosis of an autoimmune hepatitis and pancytopenia. Also associated was the onset of diabetes mellitus, found at necropsy to be related to pancreatic islet amyloid deposition. This case reinforces the view that Weber-Christian panniculitis may be an adipose response to a variety of immunological stimuli.

Citing Articles

Pfeifer-Weber-Christian Disease: A Case Report and Review of Literature on Visceral Involvements and Treatment Choices.

Rotondo C, Corrado A, Mansueto N, Cici D, Corsi F, Pennella A Clin Med Insights Case Rep. 2020; 13:1179547620917958.

PMID: 32528225 PMC: 7263116. DOI: 10.1177/1179547620917958.

Skin Manifestations Associated with Autoimmune Liver Diseases: a Systematic Review.

Beretta-Piccoli B, Invernizzi P, Gershwin M, Mainetti C Clin Rev Allergy Immunol. 2017; 53(3):394-412.

PMID: 28993983 DOI: 10.1007/s12016-017-8649-9.

Ulcerative colitis associated with Weber-Christian panniculitis and musculitis: a case report.

Nozue M, Ono A, Goto N J Gastroenterol. 1994; 29(1):84-7.

PMID: 8199701 DOI: 10.1007/BF01229080.

Cyclophosphamide-induced remission in Weber-Christian panniculitis.

Kirch W, Duhrsen U, Hoensch H, Ohnhaus E Rheumatol Int. 1985; 5(5):239-40.

PMID: 4070926 DOI: 10.1007/BF00541342.

Weber-Christian panniculitis and chronic active hepatitis.

Edge J, Dunger D, Dillon M Eur J Pediatr. 1986; 145(3):227-9.

PMID: 3769982 DOI: 10.1007/BF00446074.

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