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Cyclophosphamide-induced Remission in Weber-Christian Panniculitis

Overview
Journal Rheumatol Int
Specialty Rheumatology
Date 1985 Jan 1
PMID 4070926
Citations 3
Authors
W Kirch
U Duhrsen
H Hoensch
E Ohnhaus
Affiliations
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Abstract

A patient with Weber-Christian panniculitis is described in this report in which treatment with prednisone and hydroxychloroquine caused no improvement of the disease, and even led to a worsening of the symptoms. In contrast, administration of oral cyclophosphamide led to a rapid remission of the disease. As Weber-Christian disease has no known aetiology and no specific treatment has been established, the successful therapy with the cytostatic drug cyclophosphamide may shed light on the pathogenesis of Weber-Christian panniculitis.

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