Creutzfeldt-Jakob Disease: Further Similarities with Kuru
Overview
Neurosurgery
Psychiatry
Authors
Affiliations
A typical case of Creutzfeldt-Jakob disease is described. Two unusual morphological features-namely, `kuru-like' plaques in the cerebellum and coarsely vacuolated neurones in the striatum-are further similarities between Creutzfeldt-Jakob disease and kuru.
Creutzfeldt-Jakob Disease Misdiagnosed as Multiple System Atrophy.
Martin N, Koga S, Appleby B, Sekiya H, Dickson D Mov Disord Clin Pract. 2023; 10(3):496-500.
PMID: 36949796 PMC: 10026315. DOI: 10.1002/mdc3.13654.
Gerstmann-Sträussler-Scheinker's disease. Electron-microscopic observations on a brain biopsy.
Schlote W, Boellaard J, Schumm F, Stohr M Acta Neuropathol. 1980; 52(3):203-11.
PMID: 7445983 DOI: 10.1007/BF00705808.
[Morbus Gerstmann-Sträussler-Scheinker. The Sch. family-a report of three cases (author's transl)].
Schumm F, Boellaard J, Schlote W, Stohr M Arch Psychiatr Nervenkr (1970). 1981; 230(3):179-96.
PMID: 7295008 DOI: 10.1007/BF00344444.
Familial cerebral amyloidosis and spongiform encephalopathy.
Adam J, Crow T, DUCHEN L, Scaravilli F, Spokes E J Neurol Neurosurg Psychiatry. 1982; 45(1):37-45.
PMID: 7038052 PMC: 491262. DOI: 10.1136/jnnp.45.1.37.
Mizutani T, Okumura A, Oda M, Shiraki H J Neurol Neurosurg Psychiatry. 1981; 44(2):103-15.
PMID: 7012278 PMC: 490840. DOI: 10.1136/jnnp.44.2.103.