Acute Intermittent Porphyria Presenting with Posterior Reversible Encephalopathy Syndrome, Reversible Cerebral Vasoconstriction Syndrome and Myocardial Ischemia: A Case Report and Review

Overview

Journal Psychol Res Behav Manag

Publisher Dove Medical Press

Specialty Social Sciences

Date 2024 Aug 14

PMID 39139849

Authors

Bin Zhang

Chunqing Bu

YuYing Zhao

Zhangyong Xia

Affiliations

Soon will be listed here.

Abstract

Acute intermittent porphyria is a rare autosomal dominant metabolic disorder. It can affect the autonomic, peripheral, and central nervous system. The present study reports on the case of 28-year-old Chinese female patient with posterior reversible encephalopathy syndrome, reversible cerebral vasoconstriction syndrome and myocardial ischemia which have been very rarely reported in patients with acute intermittent porphyria.

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