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Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome

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Specialty Critical Care
Date 2022 Jul 15
PMID 35836628
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Abstract

Acute intermittent porphyria (AIP) is a rare condition that needs to be kept in mind where its early recognition, conservative management, and removal of the precipitating factor are the key factors in its management. This "little imitator" presented with varied symptoms is often misdiagnosed. The diagnosis requires a strong index of suspicion as choosing an antiepileptic medication in the management of seizure requires a judicial choice to avoid precipitation of the underlying illness. Sharma SR, Sharma N, Synmon B, Hynniewtaya Y. Porphyria-induced Postpartum Reversible Posterior Encephalopathy Syndrome. Indian J Crit Care Med 2022;26(6):728-730.

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References
1.
Zheng X, Liu X, Wang Y, Zhao R, Qu L, Pei H . Acute intermittent porphyria presenting with seizures and posterior reversible encephalopathy syndrome: Two case reports and a literature review. Medicine (Baltimore). 2018; 97(36):e11665. PMC: 6133578. DOI: 10.1097/MD.0000000000011665. View

2.
Lakhotia M, Pahadiya H, Singh J, Bhansali S, Choudhary S, Jangid H . Posterior reversible encephalopathy syndrome as a rare presenting feature of acute intermittent porphyria. Neurol India. 2015; 63(4):607-9. DOI: 10.4103/0028-3886.162081. View

3.
Dagens A, Gilhooley M . Acute intermittent porphyria leading to posterior reversible encephalopathy syndrome (PRES): a rare cause of abdominal pain and seizures. BMJ Case Rep. 2016; 2016. PMC: 4904389. DOI: 10.1136/bcr-2016-215350. View

4.
Jaramillo-Calle D, Solano J, Rabinstein A, Bonkovsky H . Porphyria-induced posterior reversible encephalopathy syndrome and central nervous system dysfunction. Mol Genet Metab. 2019; 128(3):242-253. DOI: 10.1016/j.ymgme.2019.10.011. View

5.
Kumari D, Arumilli M, Reddy L, Reddy D, Motor R . Acute Intermittent Porphyria Presenting with Posterior Reversible Encephalopathy Syndrome: A Rare Cause of Abdominal Pain and Seizures. Indian J Crit Care Med. 2020; 24(8):724-726. PMC: 7519594. DOI: 10.5005/jp-journals-10071-23532. View