Erdheim-Chester Disease with Long-standing Diabetes Insipidus and Generalized Edema

Overview

Journal Clin Case Rep

Date 2021 Oct 11

PMID 34631082

Citations 1

Authors

Faezeh Sadat Naji

Minoo Sadat Hajmiri

Zahra Mazari

Faeze Salahshour

Vahid Soleimani

Manouchehr Nakhjavani

Mahboobeh Hemmatabadi

Affiliations

Soon will be listed here.

Abstract

Erdheim-Chester disease (ECD) is a rare non-Langerhans histiocytosis. ECD is detected more frequently due to increased awareness of healthcare providers and improved diagnostic tools. This report describes a 51-year-old woman with a history of weakness, bone pain, xanthelasma palpebrarum, and diabetes insipidus. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus, bone pain, and multiorgan involvements.

Citing Articles

Erdheim-Chester disease with long-standing diabetes insipidus and generalized edema.

Naji F, Hajmiri M, Mazari Z, Salahshour F, Soleimani V, Nakhjavani M Clin Case Rep. 2021; 9(10):e04898.

PMID: 34631082 PMC: 8489502. DOI: 10.1002/ccr3.4898.

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