Hemophagocytic Lymphohistiocytosis in the Setting of HELLP Syndrome

Overview

Journal Clin Case Rep

Date 2018 Dec 20

PMID 30564350

Citations 5

Authors

Sarmen Sarkissian

Yasir Khan

Daniel Farrell

David Constable

Elizabeth Brem

Affiliations

Soon will be listed here.

Abstract

Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyper activation of the immune system. Rare cases associated with HELLP syndrome and other similar conditions in pregnancy have been reported. Despite the improved survival rates with etoposide and dexamethasone-based regimens, HLH remains a challenging disease. Experience in pregnant patients is exceedingly rare.

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Hemophagocytic lymphohistiocytosis in the setting of HELLP Syndrome.

Sarkissian S, Khan Y, Farrell D, Constable D, Brem E Clin Case Rep. 2018; 6(12):2466-2470.

PMID: 30564350 PMC: 6293182. DOI: 10.1002/ccr3.1828.

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