Uterine Didelphys Associated with Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome

Overview

Journal Radiol Case Rep

Publisher Elsevier

Specialty Radiology

Date 2016 Jun 17

PMID 27307842

Citations 11

Authors

Boram Han

Christopher N Herndon

Mitchell P Rosen

Z Jane Wang

Heike Daldrup-Link

Affiliations

Soon will be listed here.

Abstract

Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare complex of structural abnormalities of the female urogenital tract. A 17-year-old girl with uterine didelphys associated with OHVIRA syndrome presented with progressive development of cyclic lower abdominal discomfort and a large abdominopelvic mass. We describe the findings from ultrasound, computed tomography (CT), and magnetic resonance imaging (MRI), the first case report of this syndrome to examine all three different imaging modalities in a single patient. We also review the literature on OHVIRA syndrome and discuss important considerations relevant to radiologists and other clinicians.

Citing Articles

MRI Findings in a Rare Case of Left-Sided Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome in a 21-Year-Old Female.

Saifi I, Kashikar S, Parihar P, Saifi A, Ansari K Cureus. 2023; 15(10):e46704.

PMID: 38021589 PMC: 10630668. DOI: 10.7759/cureus.46704.

Herlyn-Werner-Wunderlich syndrome also known as obstructed hemivagina and ipsilateral renal anomaly: A case report and a comprehensive review of literature.

Borges A, Sanha N, Pereira H, Martins A, Costa C Radiol Case Rep. 2023; 18(8):2771-2784.

PMID: 37388267 PMC: 10300495. DOI: 10.1016/j.radcr.2023.05.024.

Obstructed hemivagina and ipsilateral renal agenesis: magnetic resonance imaging findings in young Nepali females - a report of four cases.

Paudel S, Katwal S, Kayastha P, Shrestha S, Regmi P Ann Med Surg (Lond). 2023; 85(6):3149-3154.

PMID: 37363484 PMC: 10289791. DOI: 10.1097/MS9.0000000000000904.

Herlyn-Werner-Wunderlich Syndrome: A Case Report.

Vaidya P, Agarwal P, Vaidya A JNMA J Nepal Med Assoc. 2023; 61(259):283-286.

PMID: 37203938 PMC: 10231529. DOI: 10.31729/jnma.8096.

Minimally invasive approach to Herlyn-Werner-Wunderlich syndrome with giant endometriotic cyst: a case report.

Kumar S, Dayal M, Kumar A, Singh N, Singh V Pan Afr Med J. 2023; 44:79.

PMID: 37159630 PMC: 10162894. DOI: 10.11604/pamj.2023.44.79.32667.

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