Rosai-Dorfman Disease: Report of a 3-year-old Girl with Critical Review of Treatment Options

Overview

Journal Eur J Pediatr Surg

Publisher Thieme

Specialty Pediatrics

Date 2003 Nov 18

PMID 14618531

Citations 12

Authors

V Raveenthiran

M Dhanalakshmi

P V Hayavadana Rao

P Viswanathan

Affiliations

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Abstract

Rosai-Dorfman disease (sinus histiocytosis with massive lymphadenopathy) is a newer pathological entity described in 1969. It is a self-limiting disorder of unknown aetiology. It is likely to be mistaken for lymphoma. It predominantly affects children and adolescents. However there are no publications on this disorder in the paediatric surgical literature. In this report we describe a 3-year-old girl who presented with this disease and we critically review the therapeutic options available for children. Prednisolone therapy with long-term follow-up appears to be sufficient. Surgery should be limited to biopsy and relief of compression symptoms.

Citing Articles

Rosai Dorfman Disease of Nose and Paranasal Sinuses: An Incidental Discovery.

Sagane B, Shaan M, Verma G Indian J Otolaryngol Head Neck Surg. 2024; 76(3):2881-2884.

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Histocytopathological diagnosis of Rosai-Dorfman disease: Case report.

Abraham Z, Francis Z, Ngaiza A, Kahinga A, Bukanu F Clin Case Rep. 2022; 10(2):e05412.

PMID: 35145693 PMC: 8818281. DOI: 10.1002/ccr3.5412.

Rosai-Dorfman disease of cranial and spinal origin - A case series.

Safi S, Murshed K, Ali A, Vattoth S, Haider A, Al-Bozom I Surg Neurol Int. 2020; 11:298.

PMID: 33093975 PMC: 7568110. DOI: 10.25259/SNI_391_2020.

The Rosai-Dorfman Disease: A Differential Diagnosis in Cervical Swelling.

Singh A, Kanaujiya S Indian J Otolaryngol Head Neck Surg. 2019; 71(Suppl 1):107-112.

PMID: 31741943 PMC: 6848345. DOI: 10.1007/s12070-017-1133-2.

Rosai-Dorfman disease of the subdural spine with a long segment lesion: A case report and literature review.

Tu J, Li W, Yang C J Int Med Res. 2017; 45(2):875-881.

PMID: 28173721 PMC: 5536658. DOI: 10.1177/0300060516687228.