Steroid Responsive Cutaneous Rosai-Dorfman Disease Associated with Uveitis and Hypothyroidism

Overview

Journal Clin Exp Dermatol

Publisher Oxford University Press

Specialty Dermatology

Date 2002 Jul 26

PMID 12139669

Citations 6

Authors

A Salim

M Williamson

F Barker

J Hughes

Affiliations

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Abstract

We report a patient with steroid responsive cutaneous Rosai-Dorfman disease (RDD) associated with bilateral anterior uveitis and hypothyroidism. RDD is a rare histiocytic disorder of unknown aetiology. There is characteristic histology in which large pale-staining histiocytes exhibit emperipolesis and stain positive for S-100 protein. This condition is thought to be a reactive process rather than a neoplastic one and viral and immune mediated causes have been postulated.

Citing Articles

Rosai-Dorfman disease as chronic bilateral granulomatous anterior uveitis: A case report.

Ngathaweesuk Y, Jumroendararasame C SAGE Open Med Case Rep. 2024; 12:2050313X241239528.

PMID: 38505579 PMC: 10949540. DOI: 10.1177/2050313X241239528.

Extranodal Rosai-Dorfman of the Pancreas Presents with Bilateral Granulomatous Anterior Uveitis.

Brown A, Branson S, OKeefe G Ocul Oncol Pathol. 2019; 5(4):229-233.

PMID: 31367582 PMC: 6615342. DOI: 10.1159/000493639.

Cutaneous Rosai-Dorfman Disease Confused with Vascular Mass.

Kang K, Jung S, Koh S Arch Craniofac Surg. 2017; 17(1):31-34.

PMID: 28913250 PMC: 5556720. DOI: 10.7181/acfs.2016.17.1.31.

Rosai-Dorfman disease: a report of eight cases in a tertiary care center and a review of the literature.

Maia R, De Meis E, Romano S, Dobbin J, Klumb C Braz J Med Biol Res. 2014; 48(1):6-12.

PMID: 25493377 PMC: 4288487.

Extranodal rosai-dorfman disease with cutaneous and periodontal involvement: a rare presentation.

Molina-Garrido M, Guillen-Ponce C Case Rep Oncol. 2011; 4(1):96-100.

PMID: 21475597 PMC: 3072186. DOI: 10.1159/000324760.