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Augusto B Federici

Explore the profile of Augusto B Federici including associated specialties, affiliations and a list of published articles. Areas
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Articles 86
Citations 1408
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Recent Articles
1.
Federici A, Santoro R, Santoro C, Pieri L, Santi R, Barillari G, et al.
Clin Appl Thromb Hemost . 2024 Jul; 30:10760296241264541. PMID: 39033425
Plasma-derived von Willebrand factor-containing factor VIII concentrates (pd-VWF/FVIII-C) are the mainstay of treatment in von Willebrand disease (VWD). Real-world data on efficacy and safety of these pd-VWF/FVIII-C are required. To...
2.
Federici A
Semin Thromb Hemost . 2024 Jul; 51(1):81-90. PMID: 38950597
The American Society of Hematology-International Society on Thrombosis and Haemostasis-National Hemophilia Foundation-World Federation of Hemophilia 2021 International Guidelines (IGL) on von Willebrand disease (VWD) have pointed out many challenges, mainly...
3.
OSullivan J, Tootoonchian E, Ziemele B, Makris M, Federici A, Khayat Djambas C, et al.
Haemophilia . 2023 May; 29(4):1104-1112. PMID: 37216656
Introduction: Recent guidelines for von Willebrand Disease (VWD) highlighted the challenges in diagnosis and management. Identifying the number of persons with VWD (PwVWD) internationally will help target support to aid...
4.
Pagliari M, Budde U, Baronciani L, Eshghi P, Ahmadinejad M, Badiee Z, et al.
J Thromb Haemost . 2023 Feb; 21(4):787-799. PMID: 36792472
Background: Type 3 von Willebrand disease (VWD) is the most severe form of this disease owing to the almost complete deficiency of von Willebrand factor (VWF). Replacement therapy with plasma-derived...
5.
Corrales-Medina F, Federici A, Srivastava A, Dougall A, Millar C, Roberts J, et al.
Blood Rev . 2022 Oct; 58:101018. PMID: 36210240
Von Willebrand disease (VWD) is an inherited bleeding disorder caused by quantitative or qualitative deficiencies in von Willebrand factor (VWF). People with VWD may experience excessive, recurrent or prolonged bleeding,...
6.
Berntorp E, Trakymiene S, Federici A, Holstein K, Corrales-Medina F, Pierce G, et al.
Haemophilia . 2022 Jul; 28 Suppl 5:3-15. PMID: 35861919
Introduction: The sixth Åland Islands Conference on von Willebrand disease (VWD) on the Åland Islands, Finland, was held from 20 to 22 September 2018. Aim: The meeting brought together experts...
7.
Castaman G, Borchiellini A, Coppola A, Cultrera D, Marino R, Federici A, et al.
Eur J Haematol . 2022 May; 109(2):121-128. PMID: 35531770
Objectives: The present review aims to summarize the state-of-the-art von Willebrand disease (VWD) treatment focusing on specific clinical settings (obstetrics, surgery, long-term prophylaxis and comorbidities) as well as on the...
8.
Pagliari M, Rosendaal F, Ahmadinejad M, Badiee Z, Baghaipour M, Baronciani L, et al.
J Thromb Haemost . 2022 Jan; 20(5):1106-1114. PMID: 35092343
Background: Type 3 von Willebrand disease (VWD) is a severe bleeding disorder caused by the virtually complete absence of von Willebrand factor (VWF). Pathophysiological mechanisms of VWD like defective synthesis,...
9.
Jimenez-Yuste V, Nunez L, Alvarez-Roman M, Martin-Salces M, Haya S, Federici A, et al.
Haemophilia . 2021 Nov; 28(1):e23-e27. PMID: 34735040
No abstract available.
10.
Baronciani L, Peake I, Schneppenheim R, Goodeve A, Ahmadinejad M, Badiee Z, et al.
Blood Adv . 2021 Aug; 5(15):2987-3001. PMID: 34351388
Type 3 von Willebrand disease (VWD3) is a rare and severe bleeding disorder characterized by often undetectable von Willebrand factor (VWF) plasma levels, a recessive inheritance pattern, and heterogeneous genotype....