Uncooked Cornstarch--efficacy in Type I Glycogenosis

Overview

Journal Arch Dis Child

Specialty Pediatrics

Date 1996 Jun 1

PMID 8758135

Citations 10

Authors

P J Lee

M A Dixon

J V Leonard

Affiliations

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Abstract

Uncooked cornstarch (UCCS) loads in 14 patients with type 1 glycogenosis revealed that satisfactory glycaemia was achieved for a median of 4.25 hours (range 2.5 to 6). Length of glycaemia was related weakly to UCCS dose, but not to patient age or measures of metabolic control. Careful monitoring is required during UCCS treatment.

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