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Congenital Histiocytosis X

Overview
Journal Pediatr Radiol
Specialty Pediatrics
Date 1993 Jan 1
PMID 8332403
Citations 2
Authors
A Vade
A Hayani
K L Pierce
Affiliations
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Abstract

Congenital histiocytosis X involving multiple organs is a rare disease that causes rapid mortality in intrauterine and neonatal life. The diagnosis of histiocytosis X (Letterer-Siwe disease) should be considered in a neonate with vesiculated crusting skin lesions. We present clinical, radiographic and histopathological findings in a neonate with congenital histiocytosis who died of respiratory failure due to diffuse infiltration of lungs with histiocytic cells.

Citing Articles

A Fatal Case of Congenital Langerhans Cell Histiocytosis with Disseminated Cutaneous Lesions in a Premature Neonate.

Inoue M, Tomita Y, Egawa T, Ioroi T, Kugo M, Imashuku S Case Rep Pediatr. 2016; 2016:4972180.

PMID: 27833773 PMC: 5090100. DOI: 10.1155/2016/4972180.

The sonographic appearance of lesions of the spleen and pancreas in an infant with Langerhans' cell histiocytosis.

Muwakkit S, Gharagozloo A, Souid A, Spirt B Pediatr Radiol. 1994; 24(3):222-3.

PMID: 7936807 DOI: 10.1007/BF02012200.

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