Electrocardiographic Findings in Rett Syndrome: an Explanation for Sudden Death?

Overview

Journal J Pediatr

Specialty Pediatrics

Date 1994 Jul 1

PMID 8021793

Citations 34

Authors

E A Sekul

J P Moak

R J Schultz

D G Glaze

J K Dunn

A K Percy

Affiliations

Soon will be listed here.

Abstract

Girls with Rett syndrome had significantly longer corrected QT intervals (p < 0.001) and more T-wave abnormalities (p < 0.001) than were found in age-matched healthy girls. With advancing stages of the syndrome, the proportion of corrected QT interval prolongations and T-wave changes increased. The findings suggest a possible cardiac basis for sudden, unexpected death in Rett syndrome.

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