Platelet Von Willebrand Factor in Inherited and Acquired Bleeding Disorders

Overview

Journal Proc Natl Acad Sci U S A

Specialty Science

Date 1995 Mar 28

PMID 7708659

Citations 13

Authors

P M Mannucci

Affiliations

Soon will be listed here.

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References

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Gralnick H, McKeown L, Williams S, Shafer B, Pierce L . Plasma and platelet von Willebrand factor defects in uremia. Am J Med. 1988; 85(6):806-10. DOI: 10.1016/s0002-9343(88)80025-1. View

Williams S, McKeown L, Krutzsch H, Hansmann K, Gralnick H . Purification and characterization of human platelet von Willebrand factor. Br J Haematol. 1994; 88(3):582-91. DOI: 10.1111/j.1365-2141.1994.tb05077.x. View

Gralnick H, Williams S, McKeown L, Krizek D, Shafer B, Rick M . Platelet von Willebrand factor: comparison with plasma von Willebrand factor. Thromb Res. 1985; 38(6):623-33. DOI: 10.1016/0049-3848(85)90205-1. View

Mannucci P, Lombardi R, Bader R, Vianello L, Federici A, Solinas S . Heterogeneity of type I von Willebrand disease: evidence for a subgroup with an abnormal von Willebrand factor. Blood. 1985; 66(4):796-802. View

Sporn L, Chavin S, Marder V, Wagner D . Biosynthesis of von Willebrand protein by human megakaryocytes. J Clin Invest. 1985; 76(3):1102-6. PMC: 423998. DOI: 10.1172/JCI112064. View

Gralnick H, Rick M, McKeown L, Williams S, Parker R, Maisonneuve P . Platelet von Willebrand factor: an important determinant of the bleeding time in type I von Willebrand's disease. Blood. 1986; 68(1):58-61. View

BOWIE E, Solberg Jr L, Fass D, Johnson C, Knutson G, Stewart M . Transplantation of normal bone marrow into a pig with severe von Willebrand's disease. J Clin Invest. 1986; 78(1):26-30. PMC: 329526. DOI: 10.1172/JCI112560. View

Sakariassen K, Nievelstein P, Coller B, Sixma J . The role of platelet membrane glycoproteins Ib and IIb-IIIa in platelet adherence to human artery subendothelium. Br J Haematol. 1986; 63(4):681-91. DOI: 10.1111/j.1365-2141.1986.tb07552.x. View

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Smiley R, Tittley P, Rock G . Studies on the prolonged bleeding time in von Willebrand's disease. Thromb Res. 1989; 53(5):417-26. DOI: 10.1016/0049-3848(89)90196-5. View

11.

Mannucci P, Lattuada A, Castaman G, Lombardi R, Colibretti M, Ciavarella N . Heterogeneous phenotypes of platelet and plasma von Willebrand factor in obligatory heterozygotes for severe von Willebrand disease. Blood. 1989; 74(7):2433-6. View

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Sakariassen K, Joss R, Muggli R, Kuhn H, Tschopp T, SAGE H . Collagen type III induced ex vivo thrombogenesis in humans. Role of platelets and leukocytes in deposition of fibrin. Arteriosclerosis. 1990; 10(2):276-84. DOI: 10.1161/01.atv.10.2.276. View

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Ewenstein B, Inbal A, Pober J, Handin R . Molecular studies of von Willebrand disease: reduced von Willebrand factor biosynthesis, storage, and release in endothelial cells derived from patients with type I von Willebrand disease. Blood. 1990; 75(7):1466-72. View

14.

DAlessio P, Zwaginga J, de Boer H, Federici A, Rodeghiero F, Castaman G . Platelet adhesion to collagen in subtypes of type I von Willebrand's disease is dependent on platelet von Willebrand factor. Thromb Haemost. 1990; 64(2):227-31. View

15.

Sixma J, Schiphorst M, Verweij C, Pannekoek H . Effect of deletion of the A1 domain of von Willebrand factor on its binding to heparin, collagen and platelets in the presence of ristocetin. Eur J Biochem. 1991; 196(2):369-75. DOI: 10.1111/j.1432-1033.1991.tb15826.x. View

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Castillo R, Monteagudo J, Escolar G, Ordinas A, MagallOn M, Martin Villar J . Hemostatic effect of normal platelet transfusion in severe von Willebrand disease patients. Blood. 1991; 77(9):1901-5. View

17.

Mannucci P, Tenconi P, Castaman G, Rodeghiero F . Comparison of four virus-inactivated plasma concentrates for treatment of severe von Willebrand disease: a cross-over randomized trial. Blood. 1992; 79(12):3130-7. View

18.

Rodeghiero F, Castaman G, Ruggeri M, Tosetto A . The bleeding time in normal subjects is mainly determined by platelet von Willebrand factor and is independent from blood group. Thromb Res. 1992; 65(4-5):605-15. DOI: 10.1016/0049-3848(92)90210-2. View

19.

Parker R, McKeown L, Gallin J, Gralnick H . Absence of the largest platelet-von Willebrand multimers in a patient with lactoferrin deficiency and a bleeding tendency. Thromb Haemost. 1992; 67(3):320-4. View

20.

Lattuada A, Varanukulsak P, Castaman G, Mannucci P . The response of plasma von Willebrand factor to desmopressin (DDAVP) is related to the platelet levels of von Willebrand factor. Thromb Res. 1992; 67(4):467-71. DOI: 10.1016/0049-3848(92)90276-g. View