Computed Tomography in Alexander's Disease

Overview

Journal Neuroradiology

Specialties Neurology
Radiology

Date 1980 Jan 1

PMID 7422121

Citations 11

Authors

I M Holland

B E Kendall

Affiliations

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Abstract

Two cases of biopsy-proven Alexander's disease are described with computed tomographic changes which, in our experience and on survey of the literature, have not occurred in any other condition. Such changes in a child with a progressive condition consistent with Alexander's disease. strongly support the diagnosis.

Citing Articles

Alexander disease: diagnosis with MR imaging.

van der Knaap M, Naidu S, Breiter S, Blaser S, Stroink H, Springer S AJNR Am J Neuroradiol. 2001; 22(3):541-52.

PMID: 11237983 PMC: 7976831.

A familial disorder associated with palatal myoclonus, other brainstem signs, tetraparesis, ataxia and Rosenthal fibre formation.

Howard R, Greenwood R, Gawler J, Scaravilli F, Marsden C, Harding A J Neurol Neurosurg Psychiatry. 1993; 56(9):977-81.

PMID: 8410038 PMC: 489732. DOI: 10.1136/jnnp.56.9.977.

Alexander's disease with Rosenthal fibre formation in an adult.

Walls T, Jones R, Cartlidge N, Saunders M J Neurol Neurosurg Psychiatry. 1984; 47(4):399-403.

PMID: 6726266 PMC: 1027782. DOI: 10.1136/jnnp.47.4.399.

Computed tomography in Krabbe's disease: comparison with neuropathology.

Ieshima A, Eda I, Matsui A, Yoshino K, Takashima S, Takeshita K Neuroradiology. 1983; 25(5):323-7.

PMID: 6646411 DOI: 10.1007/BF00439212.

Alexander's disease: further light-, and electron-microscopic observations.

Towfighi J, Young R, SASSANI J, RAMER J, Horoupian D Acta Neuropathol. 1983; 61(1):36-42.

PMID: 6624384 DOI: 10.1007/BF00688384.

References

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