Effect of Red Cell Transfusions, Thymic Hormone and Deoxycytidine in Severe Combined Immunodeficiency Due to Adenosine Deaminase Deficiency

Overview

Journal Clin Exp Immunol

Publisher Oxford University Press

Specialty Allergy & Immunology

Date 1982 Nov 1

PMID 6983936

Citations 2

Authors

E G Davies

R J Levinsky

D R Webster

H A Simmonds

D Perrett

Affiliations

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Citing Articles

Prenatal diagnosis of three cases of severe combined immunodeficiency: severe T cell deficiency during the first half of gestation in fetuses with adenosine deaminase deficiency.

Linch D, Levinsky R, Rodeck C, MacLennan K, Simmonds H Clin Exp Immunol. 1984; 56(2):223-32.

PMID: 6610509 PMC: 1536238.

Lymphocyte subpopulations in primary immunodeficiency disorders.

Davies E, Levinsky R, Butler M, Thomas R, Linch D Arch Dis Child. 1983; 58(5):346-51.

PMID: 6344803 PMC: 1627874. DOI: 10.1136/adc.58.5.346.

References

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Schmalstieg F, Nelson J, Mills G, Monahan T, Goldman A, Goldblum R . Increased purine nucleotides in adenosine deaminase-deficient lymphocytes. J Pediatr. 1977; 91(1):48-51. DOI: 10.1016/s0022-3476(77)80442-3. View

Simmonds H, Panayi G, Corrigall V . A role for purine metabolism in the immune response: Adenosine-deaminase activity and deoxyadenosine catabolism. Lancet. 1978; 1(8055):60-3. DOI: 10.1016/s0140-6736(78)90002-8. View

Coleman M, DOnofrio J, HUTTON J, HAHN L, Daoud A, Lampkin B . Identification and quantitation of adenine deoxynucleotides in erythrocytes of a patient with adenosine deaminase deficiency and severe combined immunodeficiency. J Biol Chem. 1978; 253(5):1619-26. View

Uberti J, LIGHTBODY J, WOLF J, ANDERSON J, Reid R, Johnson R . The effect of adenosine on mitogenesis of ADA-deficient lymphocytes. Clin Immunol Immunopathol. 1978; 10(4):446-58. DOI: 10.1016/0090-1229(78)90157-5. View

DOnofrio J, Coleman M, HUTTON J, Daoud A, Lampkin B, Dyminski J . Overproduction of adenine deoxynucleosides and deoxynucletides in adenosine deaminase deficiency with severe combined immunodeficiency disease. J Clin Invest. 1978; 62(4):884-7. PMC: 371841. DOI: 10.1172/JCI109201. View

Schmalstieg F, Mills G, Nelson J, May L, Goldman A, Goldblum R . Limited effect of erythrocyte and plasma infusions in adenosine deaminase deficiency. J Pediatr. 1978; 93(4):597-603. DOI: 10.1016/s0022-3476(78)80894-4. View

Rubinstein A, Hirschhorn R, Sicklick M, Murphy R . In vivo and in vitro effects of thymosin and adenosine deaminase on adenosine-deaminase-deficient lymphocytes. N Engl J Med. 1979; 300(8):387-92. DOI: 10.1056/NEJM197902223000802. View

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Reinherz E, Kung P, Goldstein G, Levey R, Schlossman S . Discrete stages of human intrathymic differentiation: analysis of normal thymocytes and leukemic lymphoblasts of T-cell lineage. Proc Natl Acad Sci U S A. 1980; 77(3):1588-92. PMC: 348542. DOI: 10.1073/pnas.77.3.1588. View

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Simmonds H, Levinsky R, Perrett D, Webster D . Reciprocal relationship between erythrocyte ATP and deoxy-ATP levels in inherited ADA deficiency. Biochem Pharmacol. 1982; 31(6):947-51. DOI: 10.1016/0006-2952(82)90325-2. View

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