Systemic Mastocytosis: Case Report and Literature Review

Overview

Journal J Natl Med Assoc

Publisher Elsevier

Specialty General Medicine

Date 1984 May 1

PMID 6737504

Citations 1

Authors

A H Peterson

Affiliations

Soon will be listed here.

Abstract

A case of systemic mastocytosis is reported and the literature reviewed. Although the dermatological manifestation of this rare disease, in the form of urticaria pigmentosa, is well recognized and goes along with the osteosclerotic changes that can be seen with systemic mastocytosis, it is imperative to rule out malignancy as a cause for a new onset of ascites and newly discovered sclerotic osseous changes.

Citing Articles

Systemic mastocytosis: a rare cause of osteoporosis.

Garla V, Chaudhary K, Yaqub A Pan Afr Med J. 2019; 32:169.

PMID: 31303938 PMC: 6607299. DOI: 10.11604/pamj.2019.32.169.16640.

References

Jarnum S, Zachariae H . Mastocytosis (urticaria pigmentosa) of skin, stomach, and gut with malabsorption. Gut. 1967; 8(1):64-8. PMC: 1552447. DOI: 10.1136/gut.8.1.64. View

Havard C, Scott R . Urticaria pigmentosa with visceral and skeletal lesions. Q J Med. 1959; 28:459-70. View

Mihm M, Clark W, Reed R, Caruso M . Mast cell infiltrates of the skin and the mastocytosis syndrome. Hum Pathol. 1973; 4(2):231-9. DOI: 10.1016/s0046-8177(73)80010-3. View

IVES D, Thompson D, Robinson T . Urticaria pigmentosa with spinal osteoporosis. Proc R Soc Med. 1973; 66(2):175-6. PMC: 1644485. View

Hancock B, Dandona P, Cumberland D, Jarratt J . Systemic mastocytosis--central nervous system features and lymphographic demonstration of lymph node involvement. Postgrad Med J. 1976; 52(612):659-62. PMC: 2496351. DOI: 10.1136/pgmj.52.612.659. View

Capron J, Lebrec D, Degott C, Chivrac D, Coevoet B, Delobel J . Portal hypertension in systemic mastocytosis. Gastroenterology. 1978; 74(3):595-7. View

Christophers E, Honigsmann H, Wolff K, Langner A . PUVA-treatment of urticaria pigmentosa. Br J Dermatol. 1978; 98(6):701-2. DOI: 10.1111/j.1365-2133.1978.tb03592.x. View

UVNAS B . Chemistry and storage function of mast cell granules. J Invest Dermatol. 1978; 71(1):76-80. DOI: 10.1111/1523-1747.ep12544425. View

Greaves M, Phillips C . Mast cell in disease and its pharmacologic regulation. J Invest Dermatol. 1978; 71(1):92-4. DOI: 10.1111/1523-1747.ep12544438. View

10.

Fishman R, Fleming C, Li C . Systemic mastocytosis with review of gastrointestinal manifestations. Mayo Clin Proc. 1979; 54(1):51-4. View

11.

Hirschowitz B, Groarke J . Effect of cimetidine on gastric hypersecretion and diarrhea in systemic mastocytosis. Ann Intern Med. 1979; 90(5):769-71. DOI: 10.7326/0003-4819-90-5-769. View

12.

Gerrard J, Ko C . Urticaria pigmentosa: treatment with cimetidine and chlorpheniramine. J Pediatr. 1979; 94(5):843-4. DOI: 10.1016/s0022-3476(79)80177-8. View

13.

Soter N, Austen K, Wasserman S . Oral disodium cromoglycate in the treatment of systemic mastocytosis. N Engl J Med. 1979; 301(9):465-9. DOI: 10.1056/NEJM197908303010903. View

14.

Grundfest S, Cooperman A, Ferguson R, Benjamin S . Portal hypertension associated with systemic mastocytosis and splenomegaly. Gastroenterology. 1980; 78(2):370-3. View

15.

Yam L, Yam C, Li C . Eosinophilia in systemic mastocytosis. Am J Clin Pathol. 1980; 73(1):48-54. DOI: 10.1093/ajcp/73.1.48. View

16.

Harrison P . Mastocytosis spectrum. Arch Dermatol. 1980; 116(2):158-9. View

17.

Belcon M, Collins S, Castelli M, Qizilbash A . Gastrointestinal hemorrhage in mastocytosis. Can Med Assoc J. 1980; 122(3):311-4. PMC: 1801848. View

18.

Coser P, Quaglino D, De Pasquale A, Colombetti V, Prinoth O . Cytobiological and clinical aspects of tissue mast cell leukaemia. Br J Haematol. 1980; 45(1):5-12. DOI: 10.1111/j.1365-2141.1980.tb03805.x. View

19.

Achord J, Langford H . The effect of cimetidine and propantheline on the symptoms of a patient with systemic mastocytosis. Am J Med. 1980; 69(4):610-4. DOI: 10.1016/0002-9343(80)90476-3. View

20.

Bredfeldt J, OLaughlin J, Durham J, Blessing L . Malabsorption and gastric hyperacidity in systemic mastocytosis. Results of cimetidine therapy. Am J Gastroenterol. 1980; 74(2):133-7. View