The Cytoplasmic Bodies in a Congenital Myopathy Can Be Stained with Antibodies to Desmin, the Muscle-specific Intermediate Filament Protein

Overview

Journal Acta Neuropathol

Specialty Neurology

Date 1983 Jan 1

PMID 6318501

Citations 18

Authors

M Osborn

H H Goebel

Affiliations

Soon will be listed here.

Abstract

Cytoplasmic bodies found in a muscle biopsy from a 14-year-old girl afflicted with a lifelong congenital myopathy reveal an electron-dense core surrounded by 7-10 nm filaments. Typing of the kind of intermediate filaments present shows that they are of the desmin type.

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References

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