Ectopic Functioning Adrenocortico-myelolipoma in Longstanding Nelson's Syndrome

Overview

Journal Clin Endocrinol (Oxf)

Specialty Endocrinology

Date 1979 May 1

PMID 476979

Citations 5

Authors

I Maschler

E Rosenmann

E N EHRENFELD

Affiliations

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Abstract

A 26-year-old man with the Nelson's syndrome is described, in whom an abdominal tumour developed, accompanied by recurrent Cushing's syndrome 11 years after total adrenalectomy. Upon removal the tumour was a myelolipoma containing islands of adrenocortical-like elements. On incubation of the tumour with radioactive precursors, its capacity to produce cortisol in vitro was shown. The name adrenocortico-myelolipoma is suggested for this tumour.

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