The Distribution of 17 Carbon Fatty Acids in the Liver of a Child with Propionicacidaemia

Overview

Journal Lipids

Specialty Biochemistry

Date 1971 Aug 1

PMID 4328707

Citations 4

Authors

D GOMPERTZ

Affiliations

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Citing Articles

3-hydroxypropionate: significance of -oxidation of propionate in patients with propionic acidemia and methylmalonic acidemia.

Ando T, Rasmussen K, Nyhan W, Hull D Proc Natl Acad Sci U S A. 1972; 69(10):2807-11.

PMID: 4507604 PMC: 389649. DOI: 10.1073/pnas.69.10.2807.

Odd-numbered long-chain fatty acid contents in erythrocyte membrane phospholipids in patients with an impaired propionate utilization.

Wendel U, Diekmann E, Laryea M J Inherit Metab Dis. 1988; 11 Suppl 2:225-8.

PMID: 3141708 DOI: 10.1007/BF01804242.

Asymptomatic lesions of the basal ganglia in a patient with methylmalonic aciduria.

Stockler S, Slavc I, Ebner F, Baumgartner R Eur J Pediatr. 1992; 151(12):920.

PMID: 1473551 DOI: 10.1007/BF01954135.

Propionyl-CoA carboxylase deficiency with overflow of metabolites of isoleucine catabolism at all levels.

Przyrembel H, Bremer H, Duran M, Bruinvis L, Ketting D, WADMAN S Eur J Pediatr. 1979; 130(1):1-14.

PMID: 759179 DOI: 10.1007/BF00441893.

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