Hemidystonia: a Report of 22 Patients and a Review of the Literature

Overview

Journal J Neurol Neurosurg Psychiatry

Publisher BMJ Publishing Group

Specialties Neurology
Neurosurgery
Psychiatry

Date 1985 Jul 1

PMID 4031909

Citations 53

Authors

L C Pettigrew

J Jankovic

Affiliations

Soon will be listed here.

Abstract

Hemidystonia defined as involuntary, sustained posturing of the unilateral arm, leg, and face was studied in 12 male and 10 female patients. Hemidystonia was caused by cerebrovascular disease in eight patients, perinatal trauma or childhood injury in four, head trauma and its sequelae in three, neuronal storage disorders in two, neurodegenerative disease in two, lesions after thalamotomy in two, and presumed encephalitis in one. Sixteen patients (73%) had CT evidence of contralateral basal ganglia damage, history of hemiparesis, or both. Brain damage before 7 years of age produced contralateral hemidystonia with a mean delay of 9-7 years. In older patients hemidystonia appeared within 6 months after injury. Hemidystonia may result from a disconnection between the striatum and the thalamus with relative preservation of the corticospinal pathways.

Citing Articles

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Hemidystonia secondary to pediatric thalamic glioblastoma: a case report.

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Hemiplegic Cerebral Palsy Complicated by Acute Hemidystonia in Adulthood.

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