Adrenomyeloneuropathy: Report of a Family and Electron Microscopical Findings in Peripheral Nerve

Overview

Journal J Neurol

Specialty Neurology

Date 1985 Jan 1

PMID 4020396

Citations 2

Authors

K Tanaka

A Koyama

R Koike

T Ohno

T Atsumi

T Miyatake

Affiliations

Soon will be listed here.

Abstract

A family with adrenomyeloneuropathy (AMN) is reported, whose female carriers showed severe neurological and biochemical abnormalities. Cytoplasmic lamellar inclusions were found in endoneurial cells of the biopsied sural nerve of a male patient. In spite of the peripheral nervous system involvement in patients with AMN, there have been few reports of these inclusions in the peripheral nerves of such cases.

Citing Articles

Nerve conduction studies in adrenomyeloneuropathy.

Chaudhry V, Moser H, Cornblath D J Neurol Neurosurg Psychiatry. 1996; 61(2):181-5.

PMID: 8708687 PMC: 1073993. DOI: 10.1136/jnnp.61.2.181.

Adrenoleukodystrophy in an adult female. A clinical, morphological, and neurochemical study.

Schlote W, Molzer B, PEIFFER J, Poremba M, Schumm F, Harzer K J Neurol. 1987; 235(1):1-9.

PMID: 3430177 DOI: 10.1007/BF00314189.

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