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Comprehensive Case Reports on Cardiac Manifestations in Erdheim-Chester Disease: Imaging and Clinical Insights

Overview
Journal Radiol Case Rep
Publisher Elsevier
Specialty Radiology
Date 2025 Feb 11
PMID 39931219
Authors
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Abstract

Cardiac magnetic resonance imaging (cardiac MRI) is an essential tool in the diagnosis and managing cardiac pathology. This pictorial essay discusses 3 patient case examples used in clinical practice. The cases are representative of very rarely cardiac involvement in Erdheim-Chester disease, where advanced imaging techniques play a crucial role in identifying and evaluating sporadic manifestations in the heart. Cardiac MRI is invaluable in providing detailed structural and functional information. Essential for comprehensive cardiac assessment, it is crucial in guiding effective treatment strategies and improving the patient's outcome with some of the most complex and rare cardiac conditions.

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