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Cardiopulmonary Exercise Testing in Fabry Disease: is It an Early Marker of Cardiomyopathy?

Overview
Journal Heart
Date 2025 Jan 17
PMID 39819619
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References
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De Marco O, Gambardella J, Bianco A, Fiordelisi A, Cerasuolo F, Buonaiuto A . Cardiopulmonary determinants of reduced exercise tolerance in Fabry disease. Front Cardiovasc Med. 2024; 11:1396996. PMC: 11096481. DOI: 10.3389/fcvm.2024.1396996. View

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Guazzi M, Bandera F, Ozemek C, Systrom D, Arena R . Cardiopulmonary Exercise Testing: What Is its Value?. J Am Coll Cardiol. 2017; 70(13):1618-1636. DOI: 10.1016/j.jacc.2017.08.012. View

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Del Franco A, Iannaccone G, Meucci M, Lillo R, Cappelli F, Zocchi C . Clinical staging of Anderson-Fabry cardiomyopathy: An operative proposal. Heart Fail Rev. 2023; 29(2):431-444. DOI: 10.1007/s10741-023-10370-x. View

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