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Global Trends on β-Thalassemia Research Over 10 Years: A Bibliometric Analysis

Overview
Journal Int J Gen Med
Publisher Dove Medical Press
Specialty General Medicine
Date 2024 Sep 16
PMID 39281038
Authors
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Abstract

Purpose: Thalassemia, an inherited quantitative globin disorder, is the most prevalent monogenic disease globally. While severe alpha thalassemia results in intrauterine death, β-thalassemia manifests during childhood due to the "second conversion of hemoglobin", garnering increased attention in recent decades.

Methods: In this study, a bibliometric analysis was conducted of thalassemia articles published in the Web of Science Core Collection database between 2013 and 2023 to establish a comprehensive overview and to identify emerging trends. A total of 5655 studies published between 2013 and 2023 were systematically retrieved, and annual publications demonstrated a steady increase, maintaining a high level over the past decade.

Results: The United States contributed the highest number of publications, followed by China. Notably, the journal emerged as the leading authority in β-thalassemia research. Analysis of research hotspots revealed that the pathogenesis of β-thalassemia is primarily linked to iron overload, anemia, gene mutations, and ineffective erythropoiesis. Furthermore, recent studies focusing on gene editing therapies present promising avenues for future investigation.

Conclusion: These findings grasp the research status of β-thalassemia and shed new light on future research frontiers.

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