Double-outlet Right Atrium with Double-orifice Tricuspid Valve: Report of a Rare Case and Review of the Literature
Overview
Overview
Journal
Pediatr Cardiol
Specialties
Cardiology & Vascular Diseases
Pediatrics
Pediatrics
Date
2024 Sep 14
PMID
39277555
Authors
Affiliations
Affiliations
Soon will be listed here.
Abstract
Double-outlet right atrium is an extremely rare congenital cardiac defect, in which the right atrium drains into both ventricles. Here in, we present a peculiar case involving an 8-year-old female with double-outlet right atrium characterized by three distinct atrioventricular valves and a membranous ventricular septal defect. This is associated with right atrium to left ventricular flow through the accessory atrioventricular valve while maintaining adequate size of the right ventricle. Additionally, we include a comprehensive review of the literature to underscore the variability in clinical presentation and management strategies.
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