Fibrous Dysplasia of Paranasal Sinuses with Anterior Skull-base Extension Presenting with Pneumocephalus; a Case Report

Overview

Journal Heliyon

Specialty Social Sciences

Date 2024 Jul 25

PMID 39050473

Authors

Seyed Mohammad Piri

Ahmad Pour-Rashidi

Hoda Asefi

Masume Allahmoradi

Hedieh Moradi Tabriz

Affiliations

Soon will be listed here.

Abstract

Background: Fibrous dysplasia is a benign fibro-osseous lesion where normal bone is replaced with immature dysplastic woven bone and fibrous tissue. Fibrous dysplasia has the potential to involve multiple bones of the craniofacial area in a rare condition. Management of this involvement type should be assessed carefully.

Case Report: Here, we report a 52-year-old man with progressive and bilateral frontal headache. The radio/pathologic diagnosis revealed fibrous dysplasia of paranasal sinuses with anterior skull-base extension and pneumocephalus. The patient underwent a craniotomy, and 2 weeks after the procedure, the symptoms were alleviated without any complications.

Conclusion: in case of fibrous dysplasia, patients with new onset and/or mild symptoms may have extensive lesions in multiple craniofacial bones.

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