Improvement of Diaphragmatic Excursion in the Supine Position in a Patient with Idiopathic Pleuroparenchymal Fibroelastosis: A Case Report

Overview

Journal Respir Med Case Rep

Date 2024 Jul 19

PMID 39027817

Authors

Masashi Shiraishi

Yuji Higashimoto

Osamu Nishiyama

Ryo Yamazaki

Ryuji Sugiya

Hiroki Mizusawa

Yu Takeda

Masaya Noguchi

Kengo Kanki

Mitsuo Kuwano

Tamotsu Kimura

Hisako Matsumoto

Affiliations

Soon will be listed here.

Abstract

Idiopathic pleuroparenchymal fibroelastosis (iPPFE) is a rare form of idiopathic interstitial pneumonia. We report a case of a patient with iPPFE in whom postural changes improved diaphragmatic excursion (DE) and exercise tolerance. Chest radiography showed a greater elevation of the diaphragm at maximum expiration in the supine position than the standing position. DE measured by ultrasonography was higher in the supine position than the standing position. The findings may suggest greater diaphragm movement in the supine position, leading to successful rehabilitation and improved exercise endurance. There is no effective treatment for iPPFE; therefore, an innovative treatment strategy is warranted.

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