Pulmonary Light Chain Deposition Disease: Case Series and Review of the Literature

Overview

Journal Radiol Case Rep

Publisher Elsevier

Specialty Radiology

Date 2024 Jul 10

PMID 38983277

Authors

Tomas V Gonzalez

Anja C Roden

Brian J Bartholmai

Rebecca M Lindell

Affiliations

Soon will be listed here.

Abstract

Pulmonary light chain deposition disease is a rare entity characterized by immunoglobulin deposition within the lung parenchyma with pathologic features distinct from pulmonary amyloidosis. Here, the authors present the clinical presentation, associations, and radiologic features of pulmonary light chain deposition disease in a series of 4 patients as well as discuss the distinctions from amyloidosis. The present case series highlights the frequent presence of both cysts and nodules at CT. Clinically, lymphoma and/or autoimmune disease are often associated.

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