Congenital Unilateral Pulmonary Venous Atresia with Pulmonary Veno-occlusive Disease in Contralateral Lung: an Unusual Association

Overview

Journal Pediatr Cardiol

Specialties Cardiology & Vascular Diseases
Pediatrics

Date 1986 Jan 1

PMID 3822868

Citations 4

Authors

S Shrivastava

J H MOLLER

J E Edwards

Affiliations

Soon will be listed here.

Abstract

A patient presenting with the rare association of congenital unilateral pulmonary venous atresia in one lung and pulmonary veno-occlusive disease in the other is described. The patient first presented at the age of 3 1/2 years with anemia, hemoptysis, and pulmonary hypertension. After cardiac catheterization and angiocardiography, a diagnosis of atresia of the left pulmonary veins was made for which left pneumonectomy was done. Four years later the patient presented with right-sided congestive failure and radiologic evidence of right-sided pulmonary edema from which death resulted. At autopsy, the right lung showed changes of pulmonary veno-occlusive disease, while the major veins were not involved.

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