Head and Neck Manifestations of Fibrodysplasia Ossificans Progressiva: Clinical and Imaging Findings in 2 Cases

Overview

Journal Imaging Sci Dent

Specialty Radiology

Date 2023 Oct 6

PMID 37799735

Authors

Gyu-Dong Jo

Ju-Hee Kang

Jo-Eun Kim

Won-Jin Yi

Min-Suk Heo

Sam-Sun Lee

Kyung-Hoe Huh

Affiliations

Soon will be listed here.

Abstract

Fibrodysplasia ossificans progressiva is a rare hereditary disorder characterized by progressive heterotopic ossification in muscle and connective tissue, with few reported cases affecting the head and neck region. Although plain radiographic findings and computed tomography features have been well documented, limited reports exist on magnetic resonance findings. This report presents 2 cases of fibrodysplasia ossificans progressiva, one with limited mouth opening due to heterotopic ossification of the lateral pterygoid muscle and the other with restricted neck movement due to heterotopic ossification of the platysma muscle. Clinical findings of restricted mouth opening or limited neck movement, along with radiological findings of associated heterotopic ossification, should prompt consideration of fibrodysplasia ossificans progressiva in the differential diagnosis. Dentists should be particularly vigilant with patients diagnosed with fibrodysplasia ossificans progressiva to avoid exposure to diagnostic biopsy and invasive dental procedures.

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