Recurrent Metastatic Angiosarcoma Presenting As Kasabach-Merritt Syndrome

Overview

Journal BMJ Case Rep

Specialty General Medicine

Date 2023 Jul 27

PMID 37500188

Authors

Jeyhan Boman Dhabhar

Varshil Mehta

Affiliations

Soon will be listed here.

Abstract

Angiosarcoma is an incredibly rare type of malignancy, accounting for only 1%-2% of all soft-tissue sarcomas globally. It is clinically, pathologically and radiologically difficult to diagnose angiosarcoma owing to its varied presentation with little or no well-defined imaging findings.Kasabach-Merritt syndrome is also a lesser-heard entity which carries extremely poor prognosis. It is primarily seen in infants with vascular malformations and in kaposiform haemangioendothelioma. It is a condition of consumptive coagulopathy and only few of the cases have been reported so far in the adults with a background of angiosarcoma.This report presents the case of a male in his 70s who was diagnosed with metastatic angiosarcoma and experienced a complicated disease course due to Kasabach-Merritt syndrome.

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