New Treatment Insights into Pancreatic Acinar Cell Carcinoma: Case Report and Literature Review

Overview

Journal Front Oncol

Specialty Oncology

Date 2023 Jul 19

PMID 37465113

Authors

Fangrui Zhao

Dashuai Yang

Tangpeng Xu

Jiahui He

Jin Guo

Xiangpan Li

Affiliations

Soon will be listed here.

Abstract

Pancreatic acinar cell carcinoma (PACC) is a rare pancreatic malignancy with unique clinical, molecular, and morphologic features. The long-term survival of patients with PACC is substantially better than that of patients with ductal adenocarcinoma of the pancreas. Surgical resection is considered the first choice for treatment; however, there is no standard treatment option for patients with inoperable disease. The patient with metastatic PACC reported herein survived for more than 5 years with various treatments including chemotherapy, radiotherapy, antiangiogenic therapy and combined immunotherapy.

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