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Primary Intra‑abdominal Desmoid Fibromatosis Associated with Familial Adenomatous Polyposis: A Case Report

Overview
Journal Exp Ther Med
Specialty Pathology
Date 2023 Jun 5
PMID 37273755
Authors
Lei Zhang
Yaotun Zheng
Xiaoqian Yu
Kang Yu
Shengjie Zhu
Affiliations
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Abstract

Desmoid fibromatosis (DF) is a clonal proliferative disorder of myofibroblasts, which arises, with a low incidence, in soft tissue, including within the abdomen. The incidence of DF is associated with familial adenomatous polyposis (FAP), and is more common following FAP surgery. It is rare for a patient to make his/her first visit to hospital due to DF symptoms associated with FAP. In the present report, a case of mesenteric DF associated with FAP is described. This case also had incomplete intestinal obstruction due to DF. By summarizing previous studies examining DF and FAP treatment, combined with the disease characteristics of this patient, the clinical treatment strategy for DF associated with FAP was explored.

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