Low-vision Intervention for Oculocutaneous Albinism in a Tertiary Eye Care Hospital in India

Overview

Journal Saudi J Ophthalmol

Specialty Ophthalmology

Date 2023 Mar 27

PMID 36968775

Authors

Sarika Gopalakrishnan

Kalpa Negiloni

R Vivek Suganthan

Saranya Velu

Rajiv Raman

Affiliations

Soon will be listed here.

Abstract

Purpose: The objective of this study on patients with albinism in different age groups was to compare their level of visual impairment with the low-vision intervention (LVI) and its benefit.

Methods: The medical records of 72 patients with low vision secondary to albinism who were referred to the low vision care clinic from 2015 to 2017 were analyzed. This included the demographic profile such as age, gender, occupation, ocular history, visual acuity status, and type of low-vision device (LVD) preferred. The LVDs prescribed and its subsequent improvement was compared.

Results: In this data, 70 (97.2%) people had oculocutaneous albinism and 2 (2.8%) had ocular albinism. Majority of the patients had hyperopic astigmatism 42 (58.3%) and with-the-rule astigmatism 58 (93.5%). Presenting mean visual acuity for distance was noted to be 0.88 logMAR which improved to 0.83 logMAR with the help of spectacle correction. The most commonly prescribed LVD was a dome magnifier for 15 (34.9%) patients. In all the patients, there was statistically significant improvement ( < 0.05) in near vision with the help of LVDs.

Conclusion: The study highlights the importance of appropriate LVI for each subdivided age group. Patients with albinism who have received medical and surgical treatment have no or a limited role in restoring useful vision.

Citing Articles

Colorimetric and Photobiological Properties of Light Transmitted Through Low-Vision Filters: Simulated Potential Impact on ipRGCs Responses Considering Crystalline Lens Aging.

Sanchez-Cano A, Orduna-Hospital E, Aporta J Life (Basel). 2025; 15(2).

PMID: 40003670 PMC: 11857528. DOI: 10.3390/life15020261.

Reply to letter to editor: Low-vision intervention for oculocutaneous albinism in a tertiary eye care hospital in India.

Raman R, Gopalakrishnan S, Velu S Saudi J Ophthalmol. 2024; 38(2):192.

PMID: 38988790 PMC: 11232738. DOI: 10.4103/sjopt.sjopt_304_23.

Comment on "low-vision intervention for oculocutaneous albinism in a tertiary eye care hospital in India".

Sharma N, Chaurasiya S, Singh M, Kohli P Saudi J Ophthalmol. 2024; 38(2):191.

PMID: 38988780 PMC: 11232742. DOI: 10.4103/sjopt.sjopt_282_23.

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