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» Articles » PMID: 36733686

First Described Mitral Clip in an Adult Extracardiac Fontan Patient: a Case Report

Overview
Journal Eur Heart J Case Rep
Publisher Oxford University Press
Specialty Cardiology & Vascular Diseases
Date 2023 Feb 3
PMID 36733686
Authors
Christiane L Haeffele
George K Lui
Lynn Peng
Frandics Chan
Rahul P Sharma
Affiliations
Soon will be listed here.
Abstract

Background: The use of transcatheter edge-to-edge repair (TEER) in patients with advanced heart failure has been shown to reduce hospitalizations and increase survival. As patients with Fontan circulations grow older, a significant proportion of them will develop severe atrioventricular (AV) valve regurgitation in the systemic ventricle. Conventional surgical repair and transplant carry high mortality risk for the adult Fontan patient with progressive heart failure.

Case Summary: A 51-year-old female extracardiac Fontan patient developed severe AV valve regurgitation and progressive functional decline. Based on her operative risk for conventional surgical intervention or transplant, TEER using the Abbott MitraClip device was performed. The degree of mitral regurgitation was decreased from severe to moderate regurgitation.

Discussion: This is the first known case describing the use of a successful TEER in an adult patient with an extracardiac Fontan. Given the increasing numbers of patients surviving into adulthood with a Fontan circulation, transcatheter interventions may provide an alternative treatment option to conventional surgeries and medical therapies.

Citing Articles

Transcatheter Edge-to-Edge Repair of Common Atrioventricular Valve Regurgitation in the Setting of a Lateral Tunnel Fontan Circulation.

Cordina R, Ratwatte S, Khor L, Plunkett B, Irons J, Baker D Struct Heart. 2024; 8(6):100348.

PMID: 39670043 PMC: 11632687. DOI: 10.1016/j.shj.2024.100348.

Advances in Diagnostic and Interventional Catheterization in Adults with Fontan Circulation.

Belahnech Y, Marti Aguasca G, Dos Subira L J Clin Med. 2024; 13(16).

PMID: 39200775 PMC: 11355634. DOI: 10.3390/jcm13164633.

Introduction of transcatheter edge-to-edge repair in patients with congenital heart disease at a children's hospital.

Jolley M, Sulentic A, Amin S, Gupta M, Ching S, Cianciulli A Catheter Cardiovasc Interv. 2023; 103(2):326-334.

PMID: 38149722 PMC: 10911413. DOI: 10.1002/ccd.30935.

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