The Idiopathic Hypereosinophilic Syndrome

Overview

Journal Arch Dis Child

Specialty Pediatrics

Date 1987 Jun 1

PMID 3619478

Citations 11

Authors

M A Alfaham

S D Ferguson

B Sihra

J Davies

Affiliations

Soon will be listed here.

Abstract

A 14 year old girl with idiopathic hypereosinophilic syndrome is described. In addition to weight loss, anaemia, amenorrhoea, general lethargy, anorexia, mouth ulcers, blisters of hands and feet, and petechial skin rash, she had features of involvement of the cardiovascular system as the major complication. She responded well to treatment. After a comprehensive search of the published reports 18 cases of this syndrome were identified in children under 16 years. Fifteen of these children had involvement of the cardiovascular system as the major source of their morbidity and mortality. Summary of the clinical details and laboratory, biopsy, and necropsy findings of the involvement of the various organ systems of the 18 children is presented.

Citing Articles

Bullous pemphigoid-like rash revealing hypereosinophilic syndrome.

Khallaayoune M, Sialiti S, Meziane M, Senouci K BMJ Case Rep. 2021; 14(6).

PMID: 34103306 PMC: 8189923. DOI: 10.1136/bcr-2021-242695.

Idiopathic hypereosinophilic syndrome with cutaneous involvement: a comparative review of 32 cases.

Inayat F, ONeill S, Zafar F, Marupudi S, Vasim I BMJ Case Rep. 2018; 11(1).

PMID: 30567176 PMC: 6301492. DOI: 10.1136/bcr-2018-227137.

A rare case of hypereosinophilic syndrome presenting with unilateral proptosis and torticollis.

Das J, Gupta K, Deshmukh S, Shrivastava R Indian J Ophthalmol. 2018; 66(10):1508-1511.

PMID: 30249857 PMC: 6173005. DOI: 10.4103/ijo.IJO_316_18.

A Case of Idiopathic Hypereosinophilic Syndrome Causing Mitral Valve Papillary Muscle Rupture.

Tamse T, Rampersad A, Jordan-Villegas A, Ireland J Case Rep Pediatr. 2015; 2015:538762.

PMID: 26640733 PMC: 4660015. DOI: 10.1155/2015/538762.

Idiopathic hypereosinophilic syndrome in children: 3 cases with review of literature.

Kanthila J, Bhaskaranand N Indian J Pediatr. 2012; 80(2):124-7.

PMID: 22740191 DOI: 10.1007/s12098-012-0821-x.

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