Petrified Heart in a Patient with Wolfram Syndrome

Overview

Journal J Public Health Res

Publisher Sage Publications

Specialty Public Health

Date 2022 Aug 1

PMID 35911432

Authors

Agnese Siani

Mirela Proaspatu

Giuseppe Lanzo

Paolo Irico

Sara Rodolfi

Serena Carriero

Marco Guglielmo

Affiliations

Soon will be listed here.

Abstract

Myocardial calcification is a rare complication of severe systemic sepsis. The pathophysiological mechanisms underlying calcium accumulation in cardiomyocytes in generalized sepsis are complex and still under investigation. It is a serious and life-threatening condition, usually diagnosed by autopsy, rarely with imaging techniques. We describe the case of a 38-year-old woman with Wolfram Syndrome who developed diffuse myocardial calcification during an episode of generalized sepsis.

Citing Articles

Myocardial calcification: case reports and a systematic review.

Kido T, Tanimoto K, Watanabe T, Taira M, Narita J, Ishida H Eur Heart J Imaging Methods Pract. 2024; 2(3):qyae079.

PMID: 39224618 PMC: 11367960. DOI: 10.1093/ehjimp/qyae079.

Cardiac Wolframinopathies: A Case Report of Myocarditis and a Literature Review of Cardiac Involvement in Wolfram Syndrome 1.

Villatore A, Frontino G, Cascavilla M, Vignale D, Lazzeroni D, Peretto G J Clin Med. 2024; 13(6).

PMID: 38542026 PMC: 10971342. DOI: 10.3390/jcm13061803.

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