Does the Effect of Comprehensive Respiratory Physiotherapy Home-program Differ in Children with Cystic Fibrosis and Non-cystic Fibrosis Bronchiectasis?

Overview

Journal Eur J Pediatr

Specialty Pediatrics

Date 2022 May 20

PMID 35595860

Authors

Hulya Nilgun Gurses

Hikmet Ucgun

Melih Zeren

Hilal Denizoglu Kulli

Erkan Cakir

Affiliations

Soon will be listed here.

Abstract

Conclusion: CRP is beneficial both for children with CF and NCFB and adherence to the program was high in both groups.

What Is Known: • Different physiotherapy approaches in the management of non-cystic fibrosis bronchiectasis have been based on the experience gained from the research studies performed in cystic fibrosis. • Although having similar pathophysiology, these two diseases show variation in some pulmonary and extrapulmonary features.

What Is New: • The respiratory muscle strength and the efficacy of comprehensive respiratory physiotherapy have been compared for the first time in children with cystic fibrosis and non-cystic fibrosis bronchiectasis. • Comprehensive respiratory physiotherapy provides higher increases in children with non-cystic fibrosis bronchiectasis in exercise capacity and expiratory and peripheral muscle strength; however, there was a great variability in these improvements. Nevertheless, it can be concluded that both groups significantly benefited from the CRP program.

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