Spontaneous Resolution of Congenital Dural Venous Sinus Ectasia Associated With Polymicrogyria-Case Report

Overview

Journal Front Pediatr

Specialty Pediatrics

Date 2022 Mar 17

PMID 35295696

Authors

Zuzanna Kozlowska

Paulina Komasinska

Barbara Steinborn

Kinga Tobola-Wrobel

Marek Pietryga

Marta Szymankiewicz-Breborowicz

Tomasz Szczapa

Monika Bekiesinska-Figatowska

Affiliations

Soon will be listed here.

Abstract

Dural venous sinus ectasia belongs to a rare group of venous sinus malformations of unknown origin and uncertain prognosis. We report the first patient with idiopathic congenital ectasia of the confluence of sinuses with thrombosis associated with bilateral polymicrogyria. It may highlight the causative relation between ischemia within the central nervous system due to torcular herophili ectasia with thrombosis in early pregnancy and the development of cortical malformations in neonates. We also highlight the role of MR neuroimaging in the diagnosis of these entities.

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