Uhl's Anomaly With Left Ventricular Noncompaction: Role of Multimodality Imaging in a Rare Association
Overview
Overview
Journal
JACC Case Rep
Specialty
Cardiology & Vascular Diseases
Date
2021 Sep 24
PMID
34557694
Citations
1
Authors
Affiliations
Affiliations
Soon will be listed here.
Abstract
Uhl's anomaly is a rare congenital heart disease characterized by partial or complete absence of the right ventricle myocardium. We report the first case, in a 21-year-old man, of Uhl's anomaly-associated left ventricular noncompaction. This association represents a unique clinical entity and has important implications for management strategies. ().
Citing Articles
Heart Transplantation for Uhl Anomaly in an Adult.
Toubat O, Han J, Predina J, Goldberg L, Ibrahim M JACC Case Rep. 2024; 29(10):102322.
PMID: 38601846 PMC: 11002861. DOI: 10.1016/j.jaccas.2024.102322.
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