Hepatic Sarcoidosis Resembling Primary Sclerosing Cholangitis

Overview

Journal BMJ Case Rep

Specialty General Medicine

Date 2021 Sep 8

PMID 34493554

Citations 3

Authors

Ying Chen

Camelia Ciobanu

Laurel Mohrmann

Affiliations

Soon will be listed here.

Abstract

We report the case of a 29-year-old man who presented with progressive weight loss, night sweats, abdominal pain and pruritus who was found to have obstructive jaundice and cholestatic pattern of liver injury on laboratory workup. Though findings on magnetic resonance cholangiopancreatography were initially concerning primary sclerosing cholangitis, he was ultimately diagnosed with biliary sarcoidosis after a liver biopsy. This case brings attention to the rare phenomenon of hepatic sarcoidosis causing hyperbilirubinemia and highlights the importance of reaching the correct diagnosis early, as the patient's symptoms improved after initiation of steroids.

Citing Articles

The clinical management of hepatic sarcoidosis: A systematic review.

Sinnanaidu R, Kumar V, Shunmugam R, Mahadeva S JGH Open. 2024; 8(6):e13076.

PMID: 38903487 PMC: 11187478. DOI: 10.1002/jgh3.13076.

Cirrhosis due to hepatic sarcoidosis: A rare presentation.

Islam S, Kamal I, Murshed K, Azad M Clin Case Rep. 2024; 12(6):e8999.

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Secondary sclerosing cholangitis and IgG4-sclerosing cholangitis - A review of cholangiographic and ultrasound imaging.

Moller K, Braden B, Culver E, Jenssen C, Safai Zadeh E, Alhyari A Endosc Ultrasound. 2023; 12(2):181-199.

PMID: 36588352 PMC: 10237613. DOI: 10.4103/EUS-D-22-00208.

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