Alpha 2.0
Login Register
» Articles » PMID: 34336413

Long QT-Syndrome With Torsades De Pointes Managed Considering Financial Constraints Faced by the Patient

Overview
Journal Cureus
Specialty Biomedical Engineering
Date 2021 Aug 2
PMID 34336413
Citations 2
Authors
Ramesh Patel
Sandeep Aggarwal
Pal Satyajit Singh Athwal
Sandeep Randhawa
Sukhmanii Kahlon
Affiliations
Soon will be listed here.
Abstract

Long QT syndrome (LQTS) is a rare arrhythmogenic condition characterized by abnormally long QT intervals on an electrocardiogram. The prevalence varies between 1 in 3000 and 1 in 10,000 but often remains undiagnosed. It is responsible for 3000 to 4000 sudden deaths among children and adults in the United States alone. LQTS can lead to torsades de pointes which is seen as twisting of QRS complex on electrocardiogram. We report a case of a 35-year-old patient with LQTS who presented with syncope and was found to have torsades de pointes. After acute management the patient was advised for automatic implantable cardioverter defibrillator (AICD) but because of financial constraints, she was placed on beta-blockers and permanent pacemaker.

Citing Articles

Haloperidol-induced sudden cardiac arrest in a recently detected HIV and hepatitis C patient: A unique case report.

Tamang K, Kc B, Kuikel S, Thapa S SAGE Open Med Case Rep. 2023; 11:2050313X231220792.

PMID: 38130911 PMC: 10734362. DOI: 10.1177/2050313X231220792.

Mechanical QT and JT intervals by M-mode echocardiography: An extrapolation from the concurrent electrocardiographic tracings.

Malakan Rad E, Ilali H, Majnoon M, Zeinaloo A Ann Pediatr Cardiol. 2023; 15(4):364-373.

PMID: 36935820 PMC: 10015387. DOI: 10.4103/apc.apc_169_21.

References
1.
Duggal P, Vesely M, Wattanasirichaigoon D, VILLAFANE J, Kaushik V, Beggs A . Mutation of the gene for IsK associated with both Jervell and Lange-Nielsen and Romano-Ward forms of Long-QT syndrome. Circulation. 1998; 97(2):142-6. DOI: 10.1161/01.cir.97.2.142. View
2.
Schwartz P, Crotti L, Insolia R . Long-QT syndrome: from genetics to management. Circ Arrhythm Electrophysiol. 2012; 5(4):868-77. PMC: 3461497. DOI: 10.1161/CIRCEP.111.962019. View
3.
Priori S, Wilde A, Horie M, Cho Y, Behr E, Berul C . Executive summary: HRS/EHRA/APHRS expert consensus statement on the diagnosis and management of patients with inherited primary arrhythmia syndromes. Europace. 2013; 15(10):1389-406. DOI: 10.1093/europace/eut272. View
4.
JERVELL A, LANGE-NIELSEN F . Congenital deaf-mutism, functional heart disease with prolongation of the Q-T interval and sudden death. Am Heart J. 1957; 54(1):59-68. DOI: 10.1016/0002-8703(57)90079-0. View
5.
Michael Vincent G . The long QT syndrome. Indian Pacing Electrophysiol J. 2006; 2(4):127-42. PMC: 1557415. View