Standardization of the Pathologic Diagnosis of Appendiceal Mucinous Neoplasms

Overview

Journal J Pathol Transl Med

Specialty Biomedical Engineering

Date 2021 Jul 7

PMID 34233112

Citations 11

Authors

Dong-Wook Kang

Baek-Hui Kim

Joon Mee Kim

Jihun Kim

Hee Jin Chang

Mee Soo Chang

Jin-Hee Sohn

Mee-Yon Cho

So-Young Jin

Hee Kyung Chang

Hye Seung Han

Jung Yeon Kim

Hee Sung Kim

Do Youn Park

Ha Young Park

So Jeong Lee

Wonae Lee

Hye Seung Lee

Yoo Na Kang

Younghee Choi

Affiliations

Soon will be listed here.

Abstract

Although the understanding of appendiceal mucinous neoplasms (AMNs) and their relationship with disseminated peritoneal mucinous disease have advanced, the diagnosis, classification, and treatment of AMNs are still confusing for pathologists and clinicians. The Gastrointestinal Pathology Study Group of the Korean Society of Pathologists (GPSG-KSP) proposed a multicenter study and held a workshop for the "Standardization of the Pathologic Diagnosis of the Appendiceal Mucinous Neoplasm" to overcome the controversy and potential conflicts. The present article is focused on the diagnostic criteria, terminologies, tumor grading, pathologic staging, biologic behavior, treatment, and prognosis of AMNs and disseminated peritoneal mucinous disease. In addition, GPSG-KSP proposes a checklist of standard data elements of appendiceal epithelial neoplasms to standardize pathologic diagnosis. We hope the present article will provide pathologists with updated knowledge on how to handle and diagnose AMNs and disseminated peritoneal mucinous disease.

Citing Articles

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Lower Gastrointestinal Bleeding Secondary to Appendiceal Mucinous Neoplasm: A Report of Two Cases and a Review of the Literature.

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Landscape of Genetic Mutations in Appendiceal Cancers.

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